Congenital Bleeding Disorders : Diagnosis and Management / edited by Akbar Dorgalaleh.

Format:

Book

Contributor:

Dorgalaleh, Akbar, editor.

Language:

English

Subjects (All):

Hematology.

Pediatrics.

Local Subjects:

Hematology.

Pediatrics.

Physical Description:

1 online resource (XVI, 463 p. 102 illus., 95 illus. in color.)

Edition:

2nd ed. 2023.

Place of Publication:

Cham : Springer International Publishing : Imprint: Springer, 2023.

Summary:

This significantly updated new edition describes in detail the clinical presentations, diagnosis, and management of a wide range of congenital bleeding disorders. It will assist readers in overcoming the significant challenges involved in clinical and laboratory diagnosis and in providing effective clinical care that makes optimal use of new products, including recombinant factor concentrate. The coverage ranges from hemophilia A and B and von Willebrand disease to rare bleeding disorders such as congenital factor V, factor X, factor XI, and factor XIII deficiency and inherited platelet function disorders. The exceptional attention to rarer conditions is of particular importance given the considerable risk of overlooking them during diagnosis, with potential consequences for disease-related morbidity and mortality. The authors are acknowledged specialists in the field from across the world who have particular expertise in the disorder that they discuss. The book will be of value tohematologists, oncologists, pediatricians, laboratory specialists and technicians, general physicians, and trainees.

Contents:

An Overview of Hemostasis

Congenital Bleeding Disorders: Diagnosis and Management

von Willebrand disease: an update on diagnosis and treatment

Hemophilia A, Diagnosis and Management

Hemophilia B, Diagnosis and Management

Congenital fibrinogen disorders, diagnosis, and management

Congenital Prothrombin Deficiency: Diagnosis and Management

Congenital Factor V Deficiency

Combined Factor V and Factor VIII Deficiency, Diagnosis and Management

Congenital Factor VII Deficiency, Diagnosis and Management

Vitamin K-dependent Coagulation Factors Deficiency, Diagnosis and Management

Congenital Factor X deficiency, Diagnosis and Management

Congenital Factor XI Deficiency

Congenital Factor XIII Deficiency, Diagnosis and Management

Glanzmann Thrombasthenia

Bernard-Soulier Syndrome, Diagnosis and Management

Gray Platelet Syndrome (GPS). .

Notes:

Includes bibliographical references.

ISBN:

9783031431562

3031431561