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Metabolic diseases : foundations of clinical management, genetics, and pathology / edited by Enid Gilbert-Barnes, Lewis A. Barness, Philip M. Farrell.

EBSCOhost Academic eBook Collection (North America) Available online

EBSCOhost Academic eBook Collection (North America)

Ebook Central Academic Complete Available online

Ebook Central Academic Complete
Format:
Book
Contributor:
Gilbert-Barness, Enid, 1927- editor.
Barness, Lewis A., editor.
Farrell, Philip M., editor.
Series:
IOS Press Series
Language:
English
Subjects (All):
Metabolism--Disorders.
Metabolism.
Physical Description:
1 online resource (960 pages)
Edition:
1st ed.
Place of Publication:
Amsterdam, [Netherlands] : IOS Press, 2017.
Summary:
The 2nd Edition of Metabolic Diseases provides readers with a completely updated description of the Foundations of Clinical Management, Genetics, and Pathology.A distinguished group of 31 expert authors has contributed 25 chapters as a tribute to Enid Gilbert-Barness and the late Lewis Barness--- both pioneers in this topic.
Contents:
Title Page
Preface
Foreword
About the Editors
Contents
Chapter 1: Approach to Diagnosis of Metabolic Diseases
Chapter 2: Prenatal Diagnosis and Newborn Screening
Chapter 3: Disorders of Amino Acid Metabolism
Chapter 4: Disorders of Branched Chain Amino Acid Metabolism
Chapter 5: Defects of the Urea Cycle
Chapter 6: Fatty Acid Beta-Oxidation Defects
Chapter 7: Mitochondrial Myopathies and Disorders
Chapter 8: Glycogen Storage Diseases: Diagnosis, Treatment and Outcome
Chapter 9: Mucopolysaccharidoses
Chapter 10: Oligosaccharidoses and Allied Disorders
Chapter 11: Disorders of Sterol Biosynthesis
Chapter 12: Lysosomal Storage Diseases
Chapter 13: Disorders of Nucleotide Metabolism: Purines and Pyrimidines
Chapter 14: Disorders of Metal Metabolism
Chapter 15: Neuronal Ceroid-Lipofuscinoses
Chapter 16: Cystic Fibrosis
Chapter 17: The Porphyrias
Chapter 18: Inherited Intrahepatic Cholestatic Disorders and Disorders of Bilirubin Metabolism
Chapter 19: Genetic and Metabolic Disorders of the Endocrine System
Chapter 20: Metabolic Cardiomyopathies
Chapter 21: Molecular Disorders of Red Blood Cells, Platelets, and Coagulation System
Chapter 22: Genetic Disorders of the Renal Tubule
Chapter 23: Genetic Disorders of Calcium, Phosphorus, and Bone Homeostasis
Chapter 24: Peroxisome Biogenesis Disorders
Chapter 25: Neuromuscular Disorders
Chapter 26: Gene Therapy for Metabolic Diseases
Appendix I: Newborn Screening Panel: Core Panel and Secondary Targets
Appendix II: The Metabolic Disease Autopsy
Appendix III: Laboratories Performing Specialized Studies
Subject Index
Author Index.
Notes:
Includes bibliographical references at the end of each chapters and index.
Description based on print version record.
Description based on publisher supplied metadata and other sources.
ISBN:
1-61499-718-7
OCLC:
970041845

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