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Paroxysmal movement disorders : a practical, concise guide / Kapil D. Sethi, Roberto Erro, Kailash P. Bhatia, editors.

Springer Medicine eBooks 2021 Available online

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Format:
Book
Contributor:
Sethi, Kapil D., editor.
Erro, Roberto, editor.
Bhatia, Kailash, editor.
Language:
English
Subjects (All):
Movement disorders.
Nervous system--Radiography.
Neurology.
Genre:
Electronic books.
Physical Description:
1 online resource
Place of Publication:
Cham : Springer, 2021.
System Details:
text file
PDF
Summary:
This book addresses the challenges in the differential diagnosis and management of paroxysmal movement disorders. It provides the latest information on the genetics and pathophysiology, neurophysiology and neuroimaging of the core group of disorders in the field, namely the paroxysmal dyskinesias (PxD). Focused and concise, this guide features chapters that discuss other conditions that may be paroxysmal such as, episodic ataxia, startle syndromes and other more complicated groups of paroxysmal movement disorders such as ATP1A3 spectrum disorders. A chapter on secondary (acquired) paroxysmal dyskinesia highlights medical and other disorders that may result in paroxysmal dyskinesia. The book features a particularly nuanced chapter that discusses recent discoveries in the genetic aspects of PxD, relaying that paroxysmal dyskinesias are not channelpathies, but in fact are synaptophies and transportopathies. Additionally, expertly written chapters are supplemented by high quality images, tables, and videos. Paroxysmal Movement Disorders: A Practical Guide is primarily written to educate the reader on how to make a syndromic diagnosis of paroxysmal movement disorders and how to build the diagnostic work-up accordingly, as well as how to manage patients with paroxysmal movement disorders.
Contents:
Intro
Contents
Contributors
Chapter 1: Paroxysmal Dyskinesia: Definitions and Clinical Approach
Definitions
Clinical Approach
References
Chapter 2: The Early History of Paroxysmal Dyskinesias
Earliest Descriptions of Paroxysmal Dyskinesia Were Reported as Epilepsy
Earliest Reports That These Types of Conditions Are a Paroxysmal Disorder of Involuntary Movements
Early Reports of Paroxysmal Hypnogenic Dyskinesia
Early Reports of Transient Paroxysmal Dystonia/Torticollis in Infancy
Early Reports of Paroxysmal Ataxias and Tremor
References
Chapter 3: Paroxysmal Kinesigenic Dyskinesia
PRRT2-Related PKD
PKD Associated with Other Genetic Conditions
Conclusions
Chapter 4: Paroxysmal Non-kinesigenic Dyskinesia
Introduction
Epidemiology
History
Genetics
Clinical Features
Investigations
Treatment
Conclusion
Chapter 5: Paroxysmal Exercise-Induced Dyskinesia
SLC2A1 (GLUT1)-Related Paroxysmal Dyskinesia
GCH1-Related Paroxysmal Dyskinesia
ECHS1-Related Paroxysmal Dyskinesia
Pyruvate Dehydrogenase Deficiency
Early-Onset Parkinson's Disease
Conclusions
Chapter 6: Acquired Paroxysmal Dyskinesia
Etiology
Autoimmune/Inflammatory
Endocrine/Metabolic
Hypoparathyroidism and Pseudohypoparathyroidism (HP and PHP)
Hyperthyroidism
Disorders of Glucose Metabolism
Autoimmune Disorders
Faciobrachial Dystonic Seizures (FBDS)
Vascular
Trauma
Spinal Cord Lesions
Functional (Psychogenic) Paroxysmal Dyskinesia
Miscellaneous Causes
Chapter 7: Pathophysiology of Paroxysmal Dyskinesia
PRRT2
PRRT2 Mice
PNKD
PNKD Mice
GLUT1
Glut1 Mice
Other "Dyskinetic" Genes
SCN8A
KCNMA1
Chapter 8: Neurophysiology of Paroxysmal Dyskinesia
Neurophysiology in the Diagnosis of Paroxysmal Dyskinesia
Electroencephalography
Electromyography
Other Clinical Neurophysiology Studies
Neurophysiology in the Pathophysiological Study of Paroxysmal Dyskinesia
Magnetoencephalography
Transcranial Magnetic Stimulation
Other Research Neurophysiology Studies
Chapter 9: Other Paroxysmal Movement Disorders
ADCY5 Mutations
ATP1A3 Spectrum Disorders
SCN8A Mutations
CACNA1A Mutations
SLC16A2 Mutations
Chapter 10: Functional Paroxysmal Movement Disorders
Phenotypic Characteristics
Associated Signs
Diagnosis and Treatment Approach
Chapter 11: Episodic Ataxias
EA1
EA2
EA3-EA8
Other Paroxysmal or Episodic Disorders Presenting with Ataxia
Index
Other Format:
Print version:
ISBN:
9783030537210
3030537218
OCLC:
1223058078
Access Restriction:
Restricted for use by site license.

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