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Progressive myoclonus epilepsies : state of the art / edited by Berge A. Minassian, Pasquale Striano and Giuliano Avanzini ; preface by Antonio V. Delgado-Escueta.

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Format:
Book
Contributor:
Minassian, Berge A., editor.
Striano, Pasquale, editor.
Avanzini, G., editor.
Delgado-Escueta, Antonio V., writer of preface.
Series:
Mariani Foundation paediatric neurology series ; 30.
Mariani Foundation Paediatric Neurology, 0969-0301 ; 30
Language:
English
Subjects (All):
Myoclonus.
Physical Description:
1 online resource (206 pages) : illustrations, photographs.
Edition:
1st ed.
Place of Publication:
Montrouge, France : John Libbey Eurotext, 2017.
Summary:
A comprehensive book on the current state of knowledge about this group of rare Diseases.
Contents:
PROGRESSIVE MYOCLONUS EPILEPSIES STATE OF THE ART
Foreword
Preface
Chapter 1 - The history of progressive myoclonus epilepsies
Chapter 2 - Neurophysiology of myoclonus and progressive myoclonus epilepsies
Chapter 3 - Unverricht-Lundborg disease
Chapter 4 - Lafora disease
Chapter 5 - SCARB2/LIMP2 deficiency in action myoclonus-renal failure syndrome
Chapter 6 - Neuronal ceroid lipofuscinoses
Chapter 7 - Sialidoses
Chapter 8 - Myoclonic epilepsy in mitochondrial disorders
Chapter 9 - Progressive myoclonic epilepsy associated with neuroserpin inclusion bodies (neuroserpinosis)
Chapter 10 - GOSR2: a progressive myoclonus epilepsy gene
Chapter 11 - KCTD7-related progressive myoclonic epilepsy
Chapter 12 - Autosomal recessive progressive myoclonus epilepsy due to impaired ceramide synthesis
Chapter 13 - Spinal muscular atrophy associated with progressive myoclonic epilepsy
Chapter 14 - Myoclonus epilepsy and ataxia due to potassium channel mutation (MEAK) is caused by heterozygous KCNC1 mutations
Chapter 15 - Autosomal dominant cortical tremor, myoclonus and epilepsy
Chapter 16 - Myoclonus and seizures in PMEs: pharmacology and therapeutic trials
Chapter 17 - Post-modern therapeutic approaches for progressive myoclonus epilepsy.
Notes:
Includes bibliographical references at the end of each chapters.
Description based on online resource; title from PDF title page (ebrary, viewed November 14, 2017).
ISBN:
9782742015245
2742015248
OCLC:
1007041161

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