Orphan lung diseases : a clinical guide to rare lung disease / Vincent Cottin, Jean-Francois Cordier, Luca Richeldi, editors.

Format:

Book

Contributor:

Cottin, Vincent, editor.

Cordier, J-F. (Jean-Francois), editor.

Richeldi, L., editor.

Language:

English

Subjects (All):

Lungs--Diseases.

Lungs.

Rare diseases.

Genre:

Electronic books.

Physical Description:

1 online resource (xx, 580 pages) : color illustrations

Place of Publication:

London : Springer, 2015.

System Details:

Mode of access: World Wide Web.

text file

Summary:

Focusing on clinical practice, this book explores the less common diseases affecting the airways, systematic disorders with lung involvement, interstitial lung diseases and many other orphan conditions of the lungs. It helps the reader to diagnose and manage these rare orphan diseases. Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease is a practical, informative book written by a team of international authors with much experience in rare pulmonary diseases. Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease provides synthesized and easily accessible information about the main orphan lung diseases, to aid clinicians in charge of patients with rare disease, or who consider the diagnosis of a rare disease in their patient.

Contents:

1. Orphan Lung Diseases: From definition to organisation of Care

2. The Challenge of clinical research in orphan lung diseases

3. Chronic bronchiolitis in adults

4. Diffuse bronchiectasis of genetic origin

5. Allergic bronchopulmonary mycosis

6. Orphan Tracheopathies

7. Amyloidosis and the respiratory tract

8. Churg-Strauss syndrome: A clinical and therapeutic approach

9. Granunomatosis with polyangiitis (Wegener?s granylomatosis)

10. Alveolar Hemorrhage

11. Pulmonary Involvement in Takayasu Arteritis and Behçet Disease

12. Pulmonary vascular manifestations of hereditary hemorrhagic

13. Hepatopulmonary syndrome

14. Non-Langerhans cell histiocytosis -including Erdheim-Chester disease- and the lung

15. Idiopathic eosinophilic pneumonia

16. Multiple cystic lung disease

17. Lymphangioleiomyomatosis

18. Pulmonary alveolar Proteinosis

19. Exogenous lipoid pneumonia

20. Pulmonary alveolar microlithiasis

21. Pulmonary Fibrosis and the many faces of UIP

22. The syndrome of combined pulmonary fibrosis and emphysema

23. Non-specific, Unclassifiable, and Rare Idiopathic Interstitial Pneumonia

24. Organizing Pneumonias

25. Interstitial lung disease in systemic sclerosis

26. Interstitial lung disease in connective tissue diseases other than systemic sclerosis

27. Interstitial Lung Disease in Undifferentiated Forms of Connective Tissue Disease

28. Langerhans cell Granulomatosis and smoking-related interstitial lung diseases

29. Rare causes and the spectrum of hypersensitivity penumonitis

30. Chronic beryllium disease and other insterstitial lung diseases of occupational origin

31. Lymphoproliferative lung disorders

32. Pulmonary manifestations of hematological malignancies

33. Pulmonary hypertension in orphan lung diseases

34. Orphan and rare drug-induced and iatrogenic respiratory disease

35. From cancer mimicking orphan lung disease to orphan thoracic oncology

36. Rare Diffuse lung diseases of genetic origin.

Notes:

Includes index.

Textbook.

Print version record.

Includes bibliographical references at the end of each chapters and index.

ISBN:

9781447124016

1447124014

OCLC:

900158263

Access Restriction:

Restricted for use by site license.